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Pentalogía de Cantrell: Reporte de un caso
Autores: Landeta G. Jacqueline, Eduardo Carrillo..
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Resumen:
La pentalogía de Cantrell es un raro sindrome caracterizado por presentar cinco características las cuales corresponden a un defecto esternal inferior, diafragmático anterior, pericárdico diafragmático, de la pared abdominal y alteraciones cardiacas. Se describe un caso encontrado en el Hospital Gineco Obstetrico Isidro Ayora el cual fue diagnosticado ecográficamente y cuyos hallazgos se confirmaron con resonancia magnética y visualización macroscópica de los defectos durante el parto.
Palabras Claves:
Sindrome de Cantrel; Ectopia cordis; defectos de la pared toraco-abdominal.
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Abstract:
Cantrell´s Pentalogy is a rare syndrome that features five characteristics that are the following: Inferior Sternal Defect, Inferior Diaphragmatic defect, diaphragmatic pericardia defect, and abdominal wall defects and cardiac alterations The case was reported on the Obstetrics and Ginecology Hospital Isidro Ayora, which was diagnosed by ecographic means and other findings were described by MRI and macroscopic visualization of defects observed during labor.
Key Words: Cantrell's Sd; ectopic cordis; abdominal and thorax wall defects.
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